47 yo male dx w/myotonic dystrophy type 2 in oct 2009. LE weakness, numbness, poor balance, burning sensation in feet. Spastic quadriparesis much worse in legs, right > left. Brain MRI negative. Cervical - diffuse enlargement of the cervical cord w/possible focal areas of enhancement @ c4-c5. Thoracic-diffuse enlargement w/multiple foci of abn T2 signal. Lumbar puncture. CSF - Cytology - neg for malignant cells. Serum IgG - 754 (n), CSF albumin 66.4 (H), Serum albumin 3.