Upper extremity involvement includes the fingers and hands
. Often both feet and hands
are involved and
both sides of the body (bilateral) are affected. It may affect one side of the body (unilateral), particularly in secondary cases. Less frequently, symptoms may also appear in the face, ears and other parts of the body.
The classic description of erythromelalgia is red, painful, warm hands or feet, brought on by
warming or hanging the limb downward, and relieved with cooling and elevation.